Pulmonary Langerhans cell granulomatosis with extrapulmonary involvement.
نویسندگان
چکیده
Pulmonary Langerhans cell granulomatosis is defined as an abnormal Langerhans cells infiltration in the lungs. Multifocal involvement is unusual, however. We report 3 cases of pulmonary Langerhans cell granulomatosis combined with either rib, thyroid or hypothalamus involvement.
منابع مشابه
Pulmonary veno-occlusive disease in pulmonary Langerhans' cell granulomatosis.
This report describes unusual clinical and pathological findings in a 29-yr-old female with pulmonary Langerhans' cell granulomatosis (LCG). During a 7-yr clinical course her condition deteriorated despite corticosteroid therapy, and she died of respiratory failure and pulmonary hypertension. At autopsy, there were widespread pulmonary veno-occlusive disease (PVOD) lesions as well as abundant a...
متن کاملLangerhans Cell Histiocytosis with Lungs and One Rib Involvement: a case report CHIEN-JEN LIN JINN-MING CHANG WEN-SHENG TZENG
Pulmonary Langerhans cell histiocytosis (LCH) is a rare disease. The typical findings on chest computed tomography (CT) of this disease are multiple bizarre cystic spaces associated with small peribronchiolar nodules, predominantly in the upper third of both lungs. The peribronchiolar nodules are not always present due to the evolution sequence. For patients with histiologically proven extrapul...
متن کاملPrimary pulmonary lymphoma.
Three distinct entities are now covered by the definition of primary pulmonary clonal lymphoid proliferation. The aim of this review is to describe the pathophysiological, diagnostic, prognostic and therapeutic aspects of these three entities. Low-grade pulmonary B-cell lymphoma is the most frequent form of primary pulmonary clonal lymphoid proliferation. It arises from mucosa-associated lympho...
متن کاملPulmonary Hypertension in Pulmonary Langerhans Cell Granulomatosis
Introduction. Pulmonary Langerhans cell granulomatosis is a rare disease with a variable course. In pulmonary Langerhans cell granulomatosis pulmonary hypertension is frequent and has an independent prognostic impact. A vasculopathy which ist not related to ventilatory disturbance and fibrosis has been identified. An arteriopathy and even a venulopathy have been described. Due to this possible ...
متن کاملNecrotizing sarcoid granulomatosis with extrapulmonary involvement.
Pulmonary lesions, with sarcoid-like granulomas exhibiting noncaseous necrosis, with associated granulomatous arteritis fulfil the diagnostic criteria of necrotizing sarcoid granulomatosis (NSG). We report the case of a woman who presented with recurrent headaches, transient right hemipareses and left-sided ophthalmoplegia. An excised left retro-orbital lesion demonstrated sarcoid like changes,...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید
ثبت ناماگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید
ورودعنوان ژورنال:
- Journal of the Chinese Medical Association : JCMA
دوره 67 1 شماره
صفحات -
تاریخ انتشار 2004